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EHHADH

  • Official Full Name

    enoyl-CoA, hydratase/3-hydroxyacyl CoA dehydrogenase

  • Overview

    The protein encoded by this gene is a bifunctional enzyme and is one of the four enzymes of the peroxisomal beta-oxidation pathway. The N-terminal region of the encoded protein contains enoyl-CoA hydratase activity while the C-terminal region contains 3-hydroxyacyl-CoA dehydrogenase activity. Defects in this gene are a cause of peroxisomal disorders such as Zellweger syndrome. Two transcript variants encoding different isoforms have been found for this gene.
  • Synonyms

    EHHADH; enoyl-CoA, hydratase/3-hydroxyacyl CoA dehydrogenase; ECHD, enoyl Coenzyme A, hydratase/3 hydroxyacyl Coenzyme A dehydrogenase; peroxisomal bifunctional enzyme; 3 hydroxyacyl CoA dehydrogenase; 3,2 trans enoyl CoA isomerase; 3-hydroxyacyl-CoA dehydrogenase; ECHD; ECHP_HUMAN; Enoyl Coenzyme A, hydratase/3 hydroxyacyl Coenzyme A dehydrogenase; L 3 hydroxyacyl CoA dehydrogenase; L bifunctional protein, peroxisomal; L PBE; LBFP; LBP; MGC120586; MS730; PBE; PBFE; Peroxisomal enoyl CoA hydratase; 3,2-trans-enoyl-CoA isomerase; peroxisomal enoyl-CoA hydratase; L-3-hydroxyacyl-CoA dehydrogenase; L-bifunctional protein, peroxisomal; enoyl-Coenzyme A, hydratase/3-hydroxyacyl Coenzyme A dehydrogenase; L-PBE;

  • Recombinant Proteins
  • Cell & Tissue Lysates
  • Protein Pre-coupled Magnetic Beads
  • Human
  • Mouse
  • Rat
  • Rhesus Macaque
  • Zebrafish
  • E.coli
  • HEK293
  • HEK293T
  • In Vitro Cell Free System
  • Mammalian Cell
  • Mammalian cells
  • Wheat Germ
  • Flag
  • GST
  • His
  • His (Fc)
  • Avi
  • His|SUMO
  • Myc
  • DDK
  • Myc|DDK
  • N/A
  • N
Species Cat.# Product name Source (Host) Tag Protein Length Price
Human EHHADH-395H Recombinant Human EHHADH Protein, MYC/DDK-tagged HEK293 Myc/DDK
Human EHHADH-3135H Recombinant Human EHHADH Protein, GST-tagged Wheat Germ GST
Human EHHADH-6686HCL Recombinant Human EHHADH 293 Cell Lysate HEK293 N/A
Human EHHADH-1000H Recombinant Human EHHADH Protein (1-723 aa), His-SUMO-tagged E.coli His/SUMO 1-723 aa
Human EHHADH-815H Recombinant Human EHHADH Protein, His (Fc)-Avi-tagged HEK293 His (Fc)-Avi
Human EHHADH-815H-B Recombinant Human EHHADH Protein Pre-coupled Magnetic Beads HEK293
Human EHHADH-4380HF Recombinant Full Length Human EHHADH Protein, GST-tagged In Vitro Cell Free System GST 723 amino acids
Human EHHADH-1458HFL Recombinant Full Length Human EHHADH Protein, C-Flag-tagged Mammalian cells Flag
Mouse EHHADH-5062M Recombinant Mouse EHHADH Protein Mammalian Cell His
Mouse EHHADH-2688M-B Recombinant Mouse EHHADH Protein Pre-coupled Magnetic Beads HEK293
Mouse Ehhadh-6550M Recombinant Mouse Ehhadh Protein (Met1-Leu718), N-His tagged E.coli N-His Met1-Leu718
Mouse Ehhadh-2766M Recombinant Mouse Ehhadh Protein, Myc/DDK-tagged HEK293T Myc/DDK
Mouse EHHADH-2688M Recombinant Mouse EHHADH Protein, His (Fc)-Avi-tagged HEK293 His (Fc)-Avi
Rat EHHADH-2039R Recombinant Rat EHHADH Protein Mammalian Cell His
Rat EHHADH-1696R Recombinant Rat EHHADH Protein, His (Fc)-Avi-tagged HEK293 His (Fc)-Avi
Rat EHHADH-1696R-B Recombinant Rat EHHADH Protein Pre-coupled Magnetic Beads HEK293
Rhesus Macaque EHHADH-1405R Recombinant Rhesus monkey EHHADH Protein, His-tagged Mammalian Cell His
Rhesus Macaque EHHADH-1230R Recombinant Rhesus Macaque EHHADH Protein, His (Fc)-Avi-tagged HEK293 His (Fc)-Avi
Rhesus Macaque EHHADH-1230R-B Recombinant Rhesus Macaque EHHADH Protein Pre-coupled Magnetic Beads HEK293
Zebrafish EHHADH-11800Z Recombinant Zebrafish EHHADH Mammalian Cell His
  • Involved Pathway
  • Protein Function
  • Interacting Protein

EHHADH involved in several pathways and played different roles in them. We selected most pathways EHHADH participated on our site, such as Biosynthesis of antibiotics, Butanoate metabolism, Carbon metabolism, which may be useful for your reference. Also, other proteins which involved in the same pathway with EHHADH were listed below. Creative BioMart supplied nearly all the proteins listed, you can search them on our site.

Pathway Name Pathway Related Protein
Biosynthesis of antibioticsDAO;DLD;DBT;ADSL;LDHAL6A;ECHS1;CS;NME6;SDS
Butanoate metabolismOXCT1;BDH2;OXCT2;HMGCL;GAD1B;L2HGDH;ACSM4;HADHAA;ACAT2
Carbon metabolismDLAT;PGAM1B;FBP1A;GPT2L;PDHB;PC;PRPS2;GOT1;CAT
Fatty acid degradationACAT1;ACSL5;ADH1C;EHHADH;ACSL4B;ACOX3;ALDH2.2;ACSBG1;GCDHB
Fatty acid metabolismSCD;ACSL4A;SCDB;ACSBG2;ACADS;TECRB;Scd2;ACADSB;ACAA2
Lysine degradationAGXT2L2;ALDH2.1;SETDB1;EHMT1B;MLL1;ALDH7A1;HADH;COLGALT2;AADAT
Metabolic pathwaysPIGF;ITPKA;QARS;PKMA;GPIB;CYP4F14;ST3GAL6;AMY2B;PAFAH1B2
Mitochondrial LC-Fatty Acid Beta-OxidationECI1;EHHADH;CPT2;SLC25A20

EHHADH has several biochemical functions, for example, 3-hydroxyacyl-CoA dehydrogenase activity, dodecenoyl-CoA delta-isomerase activity, enoyl-CoA hydratase activity. Some of the functions are cooperated with other proteins, some of the functions could acted by EHHADH itself. We selected most functions EHHADH had, and list some proteins which have the same functions with EHHADH. You can find most of the proteins on our site.

Function Related Protein
3-hydroxyacyl-CoA dehydrogenase activityHADHAA;HADHAB;HSD17B4;HSD17B8;HSD17B10;H2-KE6;HADHA;HADH;HADHB
dodecenoyl-CoA delta-isomerase activityECI2;ECI1;PECI;EHHADH
enoyl-CoA hydratase activityHADHB;HADHA;HADHAA;EHHADH;ECHS1;HADHAB;AUH
enzyme bindingGSTM1;CUTA;UGT1A1;ATP6AP2;MDM2;NOS1;TSPAN17;SELS;SLC12A3
protein bindingINHBB;ASNS;LCORL;NR2C2AP;TSPAN15;AIDA;DSCAM;PARVG;FN1
receptor bindingHILPDA;PTK2B;FGF12B;IDUA;TNFSF18;ANG;RARA;CD70;PDGFRB

EHHADH has direct interactions with proteins and molecules. Those interactions were detected by several methods such as yeast two hybrid, co-IP, pull-down and so on. We selected proteins and molecules interacted with EHHADH here. Most of them are supplied by our site. Hope this information will be useful for your research of EHHADH.

CCDC102B; NECAB2; BHLHE40; MID1; SSNA1; TRIM27; DES

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